WEKO3
アイテム
{"_buckets": {"deposit": "c181e4e7-0ac7-4297-a85a-7a9752652813"}, "_deposit": {"created_by": 12, "id": "3923", "owners": [12], "pid": {"revision_id": 0, "type": "depid", "value": "3923"}, "status": "published"}, "_oai": {"id": "oai:iwatemed.repo.nii.ac.jp:00003923", "sets": ["32", "80"]}, "author_link": ["11902", "11904", "11905", "11903", "11901", "11906"], "item_10001_biblio_info_7": {"attribute_name": "書誌情報", "attribute_value_mlt": [{"bibliographicIssueDates": {"bibliographicIssueDate": "2014-07", "bibliographicIssueDateType": "Issued"}, "bibliographicPageEnd": "43", "bibliographicPageStart": "41", "bibliographicVolumeNumber": "34", "bibliographic_titles": [{"bibliographic_title": "日本小児腎不全学会雑誌"}]}]}, "item_10001_description_5": {"attribute_name": "抄録", "attribute_value_mlt": [{"subitem_description": "症例は生後5ヵ月の男児で、2週間前に離乳食を開始したところ嘔吐が出現し、近医にて急性胃腸炎として希釈ミルクを頻回に与えるよう指導されたが、徐々に哺乳量が減少し、活気不良となり、当院へ救急搬送された。搬送直後、心室細動を来たしたため、直ちに心肺蘇生を行った。心肺蘇生直後の検査所見では高K血症、非乏尿性の腎機能障害、著明な高尿酸血症、重度の代謝性アシドーシスを認めた。当初、高度脱水による急性腎障害(AKI)を考え、補液および持続的血液透析濾過を施行し、腎機能障害、高尿酸血症、代謝性アシドーシスは速やかに改善した。第18病日に離乳食を開始したところ嘔吐、哺乳不良を認め、再び非乏尿性の腎機能障害、高尿酸血症、代謝性アシドーシスが出現した。その後の検査でHypoxanthine-guanine phosphoribosyltransferase部分欠損症の診断に至り、診断確定後は重炭酸、アロプリノールの投与を開始し、高尿酸血症、アシドーシスは改善し、AKIもみられなかった。2歳6ヵ月の現在、発達および腎機能は正常である。", "subitem_description_type": "Abstract"}]}, "item_10001_heading_23": {"attribute_name": "見出し", "attribute_value_mlt": [{"subitem_heading_banner_headline": "医学部", "subitem_heading_headline": "小児科学", "subitem_heading_language": "ja"}]}, "item_10001_source_id_9": {"attribute_name": "ISSN", "attribute_value_mlt": [{"subitem_source_identifier": "1341-5875", "subitem_source_identifier_type": "ISSN"}]}, "item_access_right": {"attribute_name": "アクセス権", "attribute_value_mlt": [{"subitem_access_right": "metadata only access", "subitem_access_right_uri": "http://purl.org/coar/access_right/c_14cb"}]}, "item_creator": {"attribute_name": "著者", "attribute_type": "creator", "attribute_value_mlt": [{"creatorNames": [{"creatorName": "高田, 彰"}], "nameIdentifiers": [{"nameIdentifier": "11901", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "西見, 早映子"}], "nameIdentifiers": [{"nameIdentifier": "11902", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "佐々木, 慎"}], "nameIdentifiers": [{"nameIdentifier": "11903", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "古川, ひろみ"}], "nameIdentifiers": [{"nameIdentifier": "11904", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "石川, 健"}], "nameIdentifiers": [{"nameIdentifier": "11905", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "千田, 勝一"}], "nameIdentifiers": [{"nameIdentifier": "11906", "nameIdentifierScheme": "WEKO"}]}]}, "item_keyword": {"attribute_name": "キーワード", "attribute_value_mlt": [{"subitem_subject": "アシドーシス(病因,治療)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Allopurinol(治療的利用)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "*Lesch-Nyhan症候群(合併症,超音波診断,薬物療法)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "腎臓疾患(病因,超音波診断,薬物療法)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "超音波診断", "subitem_subject_scheme": "Other"}, {"subitem_subject": "*腎不全-急性(病因,診断,薬物療法)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "痛風(病因,超音波診断,薬物療法)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Uric Acid(血液)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "高尿酸血症(病因,超音波診断,薬物療法)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "アシドーシス-代謝性(病因,治療)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "高尿酸血症性腎症(病因,超音波診断,薬物療法)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "ヒト", "subitem_subject_scheme": "Other"}, {"subitem_subject": "乳児(1〜23ヶ月)", "subitem_subject_scheme": "Other"}, {"subitem_subject": "男", "subitem_subject_scheme": "Other"}]}, "item_language": {"attribute_name": "言語", "attribute_value_mlt": [{"subitem_language": "jpn"}]}, "item_resource_type": {"attribute_name": "資源タイプ", "attribute_value_mlt": [{"resourcetype": "journal article", "resourceuri": "http://purl.org/coar/resource_type/c_6501"}]}, "item_title": "Hypoxanthine-guanine phosphoribosyltransferase部分欠損症により急性腎障害を来した乳児例", "item_titles": {"attribute_name": "タイトル", "attribute_value_mlt": [{"subitem_title": "Hypoxanthine-guanine phosphoribosyltransferase部分欠損症により急性腎障害を来した乳児例"}]}, "item_type_id": "10001", "owner": "12", "path": ["32", "80"], "permalink_uri": "https://iwatemed.repo.nii.ac.jp/records/3923", "pubdate": {"attribute_name": "公開日", "attribute_value": "2014-12-19"}, "publish_date": "2014-12-19", "publish_status": "0", "recid": "3923", "relation": {}, "relation_version_is_last": true, "title": ["Hypoxanthine-guanine phosphoribosyltransferase部分欠損症により急性腎障害を来した乳児例"], "weko_shared_id": 12}
Hypoxanthine-guanine phosphoribosyltransferase部分欠損症により急性腎障害を来した乳児例
https://iwatemed.repo.nii.ac.jp/records/3923
https://iwatemed.repo.nii.ac.jp/records/39234f5abaee-328f-4b22-bfa4-7970bb461567
Item type | 学術雑誌論文 / Journal Article(1) | |||||
---|---|---|---|---|---|---|
公開日 | 2014-12-19 | |||||
タイトル | ||||||
タイトル | Hypoxanthine-guanine phosphoribosyltransferase部分欠損症により急性腎障害を来した乳児例 | |||||
言語 | ||||||
言語 | jpn | |||||
資源タイプ | ||||||
資源タイプ識別子 | http://purl.org/coar/resource_type/c_6501 | |||||
資源タイプ | journal article | |||||
アクセス権 | ||||||
アクセス権 | metadata only access | |||||
アクセス権URI | http://purl.org/coar/access_right/c_14cb | |||||
著者 |
高田, 彰
× 高田, 彰× 西見, 早映子× 佐々木, 慎× 古川, ひろみ× 石川, 健× 千田, 勝一 |
|||||
書誌情報 |
日本小児腎不全学会雑誌 巻 34, p. 41-43, 発行日 2014-07 |
|||||
ISSN | ||||||
収録物識別子タイプ | ISSN | |||||
収録物識別子 | 1341-5875 | |||||
見出し | ||||||
大見出し | 医学部 | |||||
小見出し | 小児科学 | |||||
言語 | ja |